António, MGordo, APereira, CPinto, MFFragata, IFragata, J2016-05-242016-05-242016-06Ann Thorac Surg. 2016 Jun;101(6):2370-3http://hdl.handle.net/10400.17/2507An infrequent but devastating late complication of Fontan circulation is protein-losing enteropathy (PLE), which results from unbalanced lymphatic homeostasis. Surgical decompression of the thoracic duct by redirecting its drainage to the pulmonary venous atrium has been introduced recently as a possible treatment. This report describes a single-institution experience with this innovative procedure in 2 patients with failing Fontan circulation with PLE refractory to optimized medical therapy.engHSM CAR PEDHSM ANSHSM CCTAdrenal Cortex Hormones/therapeutic useAtrioventricular Block/etiologyAtrioventricular Block/therapyAdolescentBrachiocephalic Veins/diagnostic imagingBrachiocephalic Veins/surgeryCardiac Pacing, ArtificialCombined Modality TherapyDecompression, Surgical/methodsFontan Procedure/adverse effectsHeart Atria/diagnostic imagingHeart Atria/surgeryHeart Defects, Congenital/surgeryHypoplastic Left Heart Syndrome/surgeryLymphatic System/physiopathologyNorwood ProceduresProtein-Losing Enteropathies/etiologyProtein-Losing Enteropathies/surgeryPulmonary Veins/surgeryThoracic Duct/surgeryTomography, X-Ray ComputedVasodilator Agents/therapeutic useVena Cava, Superior/surgeryjournal article10.1016/j.athoracsur.2015.08.079