Laureano, ACarvalho, RAmaro, CFreitas, ICardoso, J2015-01-142015-01-142014Case Rep Dermatol Med. 2014;2014:437085http://hdl.handle.net/10400.17/1987Phacomatosis pigmentovascularis is a rare syndrome characterized by the coexistence of a pigmented nevus and a cutaneous vascular malformation. We report a 5-year-old boy with all the typical findings of phacomatosis pigmentovascularis type Ia. Although its existence according to the traditional classification has been questioned, this case represents a very rare association of a capillary vascular malformation and a common keratinocytic nevus of the soft type.engHCC DERVascular MalformationsPhakomatosesNeurocutaneous Syndromesjournal article