Pinto, EVeiga, MSagarribay, AConceição, C2023-03-162023-03-162022-12Cureus . 2022 Dec 18;14(12):e32663.http://hdl.handle.net/10400.17/4461Tuberous sclerosis (TS) is a genetic multisystem disorder associated with the development of benign tumors in many organs. Diffuse lipomatosis, which represents the overgrowth of fatty tissue in one part of the body, is a very rare finding reported in patients with tuberous sclerosis. We describe the case of a patient with diffuse lipomatosis in the right scapular, posterior cervical and perivertebral regions, associated with a space-occupying lesion adjacent to the odontoid process of C2 that appeared to be a pseudotumor, and discuss possible relation between these entities.engCHLC NRADCHLC NCIRDiffuse LipomatosisNeuroradiologyPeriodontoid PseudotumorPhakomatosesTuberous Sclerosis.journal article10.7759/cureus.32663