Publication
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation
| dc.contributor.author | Martinho, L | |
| dc.contributor.author | Câmara, L | |
| dc.contributor.author | Batalha, S | |
| dc.contributor.author | Rodrigues, J | |
| dc.contributor.author | Carioca, F | |
| dc.contributor.author | Marques, J | |
| dc.date.accessioned | 2022-04-06T12:23:29Z | |
| dc.date.available | 2022-04-06T12:23:29Z | |
| dc.date.issued | 2022 | |
| dc.description.abstract | Hemophilia B is a coagulation disorder characterized by a deficiency of clotting factor IX. Women are often heterozygous carriers of the disease, however if their clotting factor levels are less than 60%, they may have an increased bleeding tendency. This is even higher if levels are under 40%. We presente a case of a 14-year-old female, with mild hemofilia B (hemofilia B carrier with factor IX level < 40%) who underwent a major surgery: a posterior spinal instrumentation from D6 to L1. The perioperative management was discussed, including the perioperative administration of blood products and coagulation adjuncts. This was coordinated by a multidisciplinar team (orthopedists, anesthesiologists, hematologists and nurses) to provide the best perioperative care and follow-up. Close collaboration and communication among/with the team members and the patient/family was vital throughout. | pt_PT |
| dc.description.version | info:eu-repo/semantics/publishedVersion | pt_PT |
| dc.identifier.citation | Rev Soc Port Anestesiol 2022;31(1):16-18 | pt_PT |
| dc.identifier.doi | https://dx.org/10.25751/rspa.25544 | pt_PT |
| dc.identifier.uri | http://hdl.handle.net/10400.17/4035 | |
| dc.language.iso | eng | pt_PT |
| dc.peerreviewed | yes | pt_PT |
| dc.publisher | Sociedade Portuguesa de Anestesiologia | pt_PT |
| dc.subject | CHLC ANS | pt_PT |
| dc.subject | Adolescent | pt_PT |
| dc.subject | Hemophilia B | pt_PT |
| dc.subject | Factor IX | pt_PT |
| dc.subject | Surgical Procedures, Operative | pt_PT |
| dc.title | Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation | pt_PT |
| dc.title.alternative | Abordagem Perioperatória de uma Adolescente com Hemofilia B Submetida a Instrumentação Posterior da Coluna Dorsolombar | pt_PT |
| dc.type | journal article | |
| dspace.entity.type | Publication | |
| oaire.citation.endPage | 18 | pt_PT |
| oaire.citation.issue | 1 | pt_PT |
| oaire.citation.startPage | 16 | pt_PT |
| oaire.citation.title | Revista da Sociedade Portuguesa de Anestesiologia | pt_PT |
| oaire.citation.volume | 31 | pt_PT |
| rcaap.rights | openAccess | pt_PT |
| rcaap.type | article | pt_PT |
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