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Idiopathic Inflammatory Myopathies: State of the Art on Clinical Practice Guidelines [corrected]

2018Journal article Open access
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dc.contributor.authorMeyer, A
dc.contributor.authorScirè, CA
dc.contributor.authorTalarico, R
dc.contributor.authorAlexander, T
dc.contributor.authorAmoura, Z
dc.contributor.authorAvcin, T
dc.contributor.authorBarsotti, S
dc.contributor.authorBeretta, L
dc.contributor.authorBlagojevic, J
dc.contributor.authorBurmester, G
dc.contributor.authorCavazzana, I
dc.contributor.authorCherrin, P
dc.contributor.authorDamian, L
dc.contributor.authorDoria, A
dc.contributor.authorFonseca, JE
dc.contributor.authorFurini, F
dc.contributor.authorGaletti, I
dc.contributor.authorHoussiau, F
dc.contributor.authorKrieg, T
dc.contributor.authorMaddalena, L
dc.contributor.authorLaunay, D
dc.contributor.authorCampanilho-Marques, R
dc.contributor.authorMartin, T
dc.contributor.authorMatucci-Cerinic, M
dc.contributor.authorMoinzadeh, P
dc.contributor.authorMontecucco, C
dc.contributor.authorMoraes-Fontes, MF
dc.contributor.authorMouthon, L
dc.contributor.authorNeri, R
dc.contributor.authorPaolino, S
dc.contributor.authorPiette, Y
dc.contributor.authorRednic, S
dc.contributor.authorTamirou, F
dc.contributor.authorTincani, A
dc.contributor.authorToplak, N
dc.contributor.authorBombardieri, S
dc.contributor.authorHachulla, E
dc.contributor.authorMueller-Ladner, U
dc.contributor.authorSchneider, M
dc.contributor.authorSmith, V
dc.contributor.authorVieira, A
dc.contributor.authorCutolo, M
dc.contributor.authorMosca, M
dc.contributor.authorCavagna, L
dc.date.accessioned2021-01-22T16:46:03Z
dc.date.available2021-01-22T16:46:03Z
dc.date.issued2018
dc.description.abstractIdiopathic inflammatory myopathies (IIMs) encompass a heterogeneous group of rare autoimmune diseases characterised by muscle weakness and inflammation, but in antisynthetase syndrome arthritis and interstitial lung disease are more frequent and often inaugurate the disease. Clinical practice guidelines (CPGs) have been proposed for IIMs, but they are sparse and heterogeneous. This work aimed at identifying: i) current available CPGs for IIMs, ii) patients ' and clinicians' unmet needs not covered by CPGs. It has been performed in the framework of the European Reference Network on rare and complex connective tissue and musculoskeletal diseases (ReCONNET), a network of centre of expertise and patients funded by the European Union's Health Programme. Fourteen original CPGs were identified, notably recommending that: i) extra-muscular involvements should be assessed; ii) corticosteroids and methotrexate or azathioprine are first-line therapies of IIMs. ii) IVIG is a treatment of resistant-DM that may be also used in other resistant-IIMs; iii) physical therapy and sun protection (in DM patients) are part of the treatment; v) tumour screening for patients with DM include imaging of chest, abdomen, pelvis and breast (in woman) along with colonoscopy (in patients over 50 years); vi) disease activity and damages should be monitor using standardised and validated tools. Yet, only half of these CPGs were evidence-based. Crucial unmet needs were identified both by patients and clinicians. In particular, there was a lack of large multidisciplinary working group and of patients ' preferences. The following fields were not or inappropriately targeted: diagnosis; management of extra-muscular involvements other than skin; co-morbidities and severe manifestations.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationRMD Open. 2019 Feb 26;4(Suppl 1):e000784pt_PT
dc.identifier.doi10.1136/rmdopen-2018-000784pt_PT
dc.identifier.urihttp://hdl.handle.net/10400.17/3546
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherBMJ Openpt_PT
dc.subjectIdiopathic inflammatory myopathiespt_PT
dc.subjectState of the artpt_PT
dc.subjectClinical practice guidelinespt_PT
dc.subjectHCC DAUTOIMpt_PT
dc.titleIdiopathic Inflammatory Myopathies: State of the Art on Clinical Practice Guidelines [corrected]pt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.issueSuppl 1pt_PT
oaire.citation.startPagee000784pt_PT
oaire.citation.titleRMD openpt_PT
oaire.citation.volume4pt_PT
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT

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