Publication
Perivascular Epithelioid Cell Tumor: A Case Report of a Rare Entity
| dc.contributor.author | Cardosa, MF | |
| dc.contributor.author | Ferreira de Lima, S | |
| dc.contributor.author | Knoblich, M | |
| dc.contributor.author | Afonso, I | |
| dc.contributor.author | Mendes, C | |
| dc.date.accessioned | 2022-09-05T15:00:39Z | |
| dc.date.available | 2022-09-05T15:00:39Z | |
| dc.date.issued | 2021 | |
| dc.description.abstract | Perivascular epithelioid cell tumor is a rare mesenchymal tumor with myomelanocytic differentiation. It mainly occurs in middle-aged females and can be found at any location. The differential diagnosis is broad but the immunohistochemical biomarkers establish the diagnosis. A 4-year-old girl was referred to a pediatric gastroenterology clinic due to recurrent umbilical pain and the workup revealed biliary lithiasis. She remained in follow-up, asymptomatic, no physical findings, and stable ultrasound. Six years later, a supra-umbilical mass was detected by ultrasound, and the magnetic resonance imaging revealed a highly vascularized intraperitoneal tumor with well-defined limits. Surgical mass resection was performed, and the histology revealed morphological and immunohistochemical aspects of a perivascular epithelioid cell tumor of the abdominal wall. Given the size of the lesion (> 5 cm) and admitting uncertain malignant potential, she was submitted to margin enlargement. Four years later, she remains asymptomatic without clinical or imagiological evidence of relapse. | pt_PT |
| dc.description.version | info:eu-repo/semantics/publishedVersion | pt_PT |
| dc.identifier.citation | Port J Pediatr 2021;52:59-63 | pt_PT |
| dc.identifier.uri | http://hdl.handle.net/10400.17/4239 | |
| dc.language.iso | eng | pt_PT |
| dc.peerreviewed | yes | pt_PT |
| dc.publisher | Sociedade Portuguesa de Pediatria | pt_PT |
| dc.subject | Incidental Findings | pt_PT |
| dc.subject | Perivascular Epithelioid Cell Neoplasms/diagnosis | pt_PT |
| dc.subject | Perivascular Epithelioid Cell Neoplasms/surgery | pt_PT |
| dc.subject | Abdominal Wall | pt_PT |
| dc.subject | Treatment Outcome | pt_PT |
| dc.subject | Case Report | pt_PT |
| dc.subject | HDE GAS PED | pt_PT |
| dc.subject | HDE CIR PED | pt_PT |
| dc.title | Perivascular Epithelioid Cell Tumor: A Case Report of a Rare Entity | pt_PT |
| dc.type | journal article | |
| dspace.entity.type | Publication | |
| oaire.citation.endPage | 63 | pt_PT |
| oaire.citation.startPage | 59 | pt_PT |
| oaire.citation.volume | 52 | pt_PT |
| rcaap.rights | openAccess | pt_PT |
| rcaap.type | article | pt_PT |