Publication
Neonatal Acute Compartment Syndrome as First Manifestation of Hematologic Disease: Case Report
| dc.contributor.author | Sacras, ML | |
| dc.contributor.author | Ladeira, C | |
| dc.contributor.author | Carmo, S | |
| dc.contributor.author | Kjöllerström, P | |
| dc.date.accessioned | 2022-09-14T12:21:00Z | |
| dc.date.available | 2022-09-14T12:21:00Z | |
| dc.date.issued | 2021 | |
| dc.description.abstract | Hemophilia A, characterized by deficiency of functional plasma clotting factor VIII, is an X-linked disorder. Signs and symptoms depend on factor VIII levels. Severe hemophilia A (factor levels less than 1%) is usually diagnosed in the first two years of life. Pediatric compartment syndrome is most associated with trauma, but infectious and vascular causes must also be considered. We report a case of a newborn who presented with a severe hand hematoma after venous puncture, complicated by compartment syndrome. An isolated prolonged partial thromboplastin time was found, and hemophilia was suspected. Factor VIII levels less than 1% were consistent with severe hemophilia A. The patient received recombinant factor VIII perioperatively. Fasciotomy was performed and the patient was kept on antibiotics until closure. | pt_PT |
| dc.description.version | info:eu-repo/semantics/publishedVersion | pt_PT |
| dc.identifier.citation | Port J Pediatr 2021;52:193-6 | pt_PT |
| dc.identifier.doi | doi.org/10.25754/pjp.2021.20470 | pt_PT |
| dc.identifier.uri | http://hdl.handle.net/10400.17/4247 | |
| dc.language.iso | eng | pt_PT |
| dc.peerreviewed | yes | pt_PT |
| dc.publisher | Sociedade Portuguesa de Pediatria | pt_PT |
| dc.subject | Acute Disease | pt_PT |
| dc.subject | Compartment Syndromes/ diagnosis | pt_PT |
| dc.subject | Compartment Syndromes/etiology | pt_PT |
| dc.subject | Compartment Syndromes/therapy | pt_PT |
| dc.subject | Fasciotomy; Hemophilia A/complications | pt_PT |
| dc.subject | Hemophilia A/diagnosis | pt_PT |
| dc.subject | Infant, Newborn | pt_PT |
| dc.subject | Case Report | pt_PT |
| dc.subject | HDE CIR PED | pt_PT |
| dc.subject | HDE HEM PED | pt_PT |
| dc.title | Neonatal Acute Compartment Syndrome as First Manifestation of Hematologic Disease: Case Report | pt_PT |
| dc.type | journal article | |
| dspace.entity.type | Publication | |
| oaire.citation.endPage | 196 | pt_PT |
| oaire.citation.startPage | 196 | pt_PT |
| oaire.citation.volume | 52 | pt_PT |
| rcaap.rights | openAccess | pt_PT |
| rcaap.type | article | pt_PT |