A Very Rare Case of Coronary Artery Bypass Grafting in a Progeria Child

Cerejo, R; Rodrigues, R; Martins, JD; Torres, C; Sousa, L; Pinto, MF; Fragata, J

http://hdl.handle.net/10400.17/3659

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Abstract(s)

Hutchinson-Gilford progeria syndrome is a rare genetic disorder, characterized by progressive premature aging and early death in the first or second decade of life, usually secondary to cardiovascular events (myocardial infarction and stroke). We report a case of a 14-year-old boy with progeria syndrome and cardiac arrest due to myocardial infarction, who was submitted to an immediate coronary angiography which revealed left main stem and three-vessel coronary artery disease. A prompt double bypass coronary artery grafting surgery was performed, and, despite successful coronary reperfusion, the patient remained in coma and brain death was declared on fourth day after surgery.

Keywords

Adolescent Coronary Angiography Coronary Artery Bypass Electrocardiography Heart Arrest Humans Male Myocardial Infarction Progeria Rare Diseases HSM CCT HSM CAR PED HSM CAR