Browsing by Author "Tesi, B"
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- Fatal Central Nervous System Lymphocytic Vasculitis after Treatment for Burkitt Lymphoma in a Patient with a SH2D1A MutationPublication . Neves, JF; Raga, LT; Chiang, SCC; Tesi, B; Vieira, JP; Cordeiro, AI; Borrego, L; Bryceson, YTVery rarely, patients with X-linked lymphoproliferative syndrome type 1 present central nervous system vasculitis. We report a patient carrying a SH2D1A mutation that, after treatment for lymphoma developed fatal central nervous system vasculitis. He lacked signs of ongoing Epstein-Barr virus infection. We propose that impaired T cell homeostasis caused by SAP deficiency facilitates aberrant CD8 T cell activation against vascular antigens promoting clinical manifestations.
- Hemophagocytic Lymphohistiocytosis in 2 Patients with Underlying IFN-g Receptor DeficiencyPublication . Tesi, B; Sieni, E; Neves, C; Romano, F; Cetica, V; Cordeiro, AI; Chiang, S; Schlums, H; Galli, L; Avenali, S; Tondo, A; Canessa, C; Henter, J; Nordenskjold, M; Hsu, A; Holland, S; Farela Neves, J; Azzari, C; Bryceson, Y