Successful Percutaneous Treatment with the Konar MFTM-VSD Occluder in an Infant with Abernethy Syndrome. Case Report

Loureiro, P; Georgiev, S; Ewert, P; Tanase, D; Eicken, A; Kammer, B; Dalla-Pozza, R

http://hdl.handle.net/10400.17/4638

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Abstract(s)

Cyanosis persisting after surgical repair of complex congenital heart disease (CHD) may be related to the underlying disease. However, extracardiac causes should be also considered. We report on a patient with heterotaxy syndrome and double outlet right ventricle, in whom postoperative cyanosis was associated with an Abernethy malformation type II causing a hepatopulmonary syndrome. Despite this complex anatomy, interventional closure of the portosystemic shunt was done with a Konar MF™-VSD Occluder. The patient recovered rapidly with relief of cyanosis within one month. This case highlights the importance of a careful diagnostic assessment in patients with complex CHD, who presents cyanoses after surgical repair. In addition, it shows the feasibility and safety of a percutaneous approach with complete closure of the vascular malformation in a patient with a complex anatomy.