Publication
Successful Percutaneous Treatment with the Konar MFTM-VSD Occluder in an Infant with Abernethy Syndrome. Case Report
dc.contributor.author | Loureiro, P | |
dc.contributor.author | Georgiev, S | |
dc.contributor.author | Ewert, P | |
dc.contributor.author | Tanase, D | |
dc.contributor.author | Eicken, A | |
dc.contributor.author | Kammer, B | |
dc.contributor.author | Dalla-Pozza, R | |
dc.date.accessioned | 2023-08-11T14:08:02Z | |
dc.date.available | 2023-08-11T14:08:02Z | |
dc.date.issued | 2021 | |
dc.description.abstract | Cyanosis persisting after surgical repair of complex congenital heart disease (CHD) may be related to the underlying disease. However, extracardiac causes should be also considered. We report on a patient with heterotaxy syndrome and double outlet right ventricle, in whom postoperative cyanosis was associated with an Abernethy malformation type II causing a hepatopulmonary syndrome. Despite this complex anatomy, interventional closure of the portosystemic shunt was done with a Konar MF™-VSD Occluder. The patient recovered rapidly with relief of cyanosis within one month. This case highlights the importance of a careful diagnostic assessment in patients with complex CHD, who presents cyanoses after surgical repair. In addition, it shows the feasibility and safety of a percutaneous approach with complete closure of the vascular malformation in a patient with a complex anatomy. | pt_PT |
dc.description.version | info:eu-repo/semantics/publishedVersion | pt_PT |
dc.identifier.citation | Cardiovasc Diagn Ther . 2021 Apr;11(2):631-636. | pt_PT |
dc.identifier.doi | 10.21037/cdt-20-380 | pt_PT |
dc.identifier.uri | http://hdl.handle.net/10400.17/4638 | |
dc.language.iso | eng | pt_PT |
dc.peerreviewed | yes | pt_PT |
dc.publisher | AME Publishing | pt_PT |
dc.subject | HSM CAR PED | pt_PT |
dc.subject | Abernethy Malformation | pt_PT |
dc.subject | Congenital Heart Disease | pt_PT |
dc.subject | Cyanosis | pt_PT |
dc.subject | Hepatopulmonary Syndrome | pt_PT |
dc.title | Successful Percutaneous Treatment with the Konar MFTM-VSD Occluder in an Infant with Abernethy Syndrome. Case Report | pt_PT |
dc.type | journal article | |
dspace.entity.type | Publication | |
oaire.citation.endPage | 636 | pt_PT |
oaire.citation.issue | 2 | pt_PT |
oaire.citation.startPage | 631 | pt_PT |
oaire.citation.title | Cardiovascular Diagnosis and Therapy | pt_PT |
oaire.citation.volume | 11 | pt_PT |
rcaap.rights | openAccess | pt_PT |
rcaap.type | article | pt_PT |