Repository logo
 
Publication

Successful Percutaneous Treatment with the Konar MFTM-VSD Occluder in an Infant with Abernethy Syndrome. Case Report

dc.contributor.authorLoureiro, P
dc.contributor.authorGeorgiev, S
dc.contributor.authorEwert, P
dc.contributor.authorTanase, D
dc.contributor.authorEicken, A
dc.contributor.authorKammer, B
dc.contributor.authorDalla-Pozza, R
dc.date.accessioned2023-08-11T14:08:02Z
dc.date.available2023-08-11T14:08:02Z
dc.date.issued2021
dc.description.abstractCyanosis persisting after surgical repair of complex congenital heart disease (CHD) may be related to the underlying disease. However, extracardiac causes should be also considered. We report on a patient with heterotaxy syndrome and double outlet right ventricle, in whom postoperative cyanosis was associated with an Abernethy malformation type II causing a hepatopulmonary syndrome. Despite this complex anatomy, interventional closure of the portosystemic shunt was done with a Konar MF™-VSD Occluder. The patient recovered rapidly with relief of cyanosis within one month. This case highlights the importance of a careful diagnostic assessment in patients with complex CHD, who presents cyanoses after surgical repair. In addition, it shows the feasibility and safety of a percutaneous approach with complete closure of the vascular malformation in a patient with a complex anatomy.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationCardiovasc Diagn Ther . 2021 Apr;11(2):631-636.pt_PT
dc.identifier.doi10.21037/cdt-20-380pt_PT
dc.identifier.urihttp://hdl.handle.net/10400.17/4638
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherAME Publishingpt_PT
dc.subjectHSM CAR PEDpt_PT
dc.subjectAbernethy Malformationpt_PT
dc.subjectCongenital Heart Diseasept_PT
dc.subjectCyanosispt_PT
dc.subjectHepatopulmonary Syndromept_PT
dc.titleSuccessful Percutaneous Treatment with the Konar MFTM-VSD Occluder in an Infant with Abernethy Syndrome. Case Reportpt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.endPage636pt_PT
oaire.citation.issue2pt_PT
oaire.citation.startPage631pt_PT
oaire.citation.titleCardiovascular Diagnosis and Therapypt_PT
oaire.citation.volume11pt_PT
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT

Files

Original bundle
Now showing 1 - 1 of 1
Loading...
Thumbnail Image
Name:
Card Diagn Ther 2021.pdf
Size:
1.79 MB
Format:
Adobe Portable Document Format
License bundle
Now showing 1 - 1 of 1
No Thumbnail Available
Name:
license.txt
Size:
1.71 KB
Format:
Item-specific license agreed upon to submission
Description: