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X-Linked Agammaglobulinemia (XLA):Phenotype, Diagnosis, and Therapeutic Challenges Around the World

dc.contributor.authorEl-Sayed, ZA
dc.contributor.authorAbramova, I
dc.contributor.authorAldave, JC
dc.contributor.authorAl-Herz, W
dc.contributor.authorBezrodnik, L
dc.contributor.authorBoukari, R
dc.contributor.authorBousfiha, AA
dc.contributor.authorCancrini, C
dc.contributor.authorCondino-Neto, A
dc.contributor.authorDbaibo, G
dc.contributor.authorDerfalvi, B
dc.contributor.authorDogu, Fi
dc.contributor.authorEdgar, JDM
dc.contributor.authorEley, B
dc.contributor.authorEl-Owaidy, RH
dc.contributor.authorEspinosa-Padilla, SE
dc.contributor.authorGalal, N
dc.contributor.authorHaerynck, F
dc.contributor.authorHanna-Wakim, R
dc.contributor.authorHossny, E
dc.contributor.authorIkinciogullari, A
dc.contributor.authorKamal, E
dc.contributor.authorKanegane, H
dc.contributor.authorKechout, N
dc.contributor.authorLau, YL
dc.contributor.authorMorio, T
dc.contributor.authorMoschese, V
dc.contributor.authorNeves, JF
dc.contributor.authorOuederni, M
dc.contributor.authorPaganelli, R
dc.contributor.authorParis, K
dc.contributor.authorPignata, C
dc.contributor.authorPlebani, A
dc.contributor.authorQamar, FN
dc.contributor.authorQureshi, S
dc.contributor.authorRadhakrishnan, N
dc.contributor.authorRezaei, N
dc.contributor.authorRosario, N
dc.contributor.authorRoutes, J
dc.contributor.authorSanchez, B
dc.contributor.authorSediva, A
dc.contributor.authorSeppanen, MR
dc.contributor.authorSerrano, EG
dc.contributor.authorShcherbina, A
dc.contributor.authorSingh, S
dc.contributor.authorSiniah, S
dc.contributor.authorSpadaro, G
dc.contributor.authorTang, M
dc.contributor.authorVinet, AM
dc.contributor.authorVolokha, A
dc.contributor.authorSullivan, KE
dc.date.accessioned2019-04-10T10:28:36Z
dc.date.available2019-04-10T10:28:36Z
dc.date.issued2019
dc.description.abstractX-linked agammaglobulinemia is an inherited immunodeficiency recognized since 1952. In spite of seven decades of experience, there is still a limited understanding of regional differences in presentation and complications. This study was designed by the Primary Immunodeficiencies Committee of the World Allergy Organization to better understand regional needs, challenges and unique patient features.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationWorld Allergy Organ J. 2019 Mar 22;12(3):100018pt_PT
dc.identifier.doi10.1016/j.waojou.2019.100018pt_PT
dc.identifier.urihttp://hdl.handle.net/10400.17/3249
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherElsevierpt_PT
dc.subjectAgammaglobulinemiapt_PT
dc.subjectAutoimmunitypt_PT
dc.subjectChronic Lung Diseasept_PT
dc.subjectFamily Historypt_PT
dc.subjectGastrointestinalpt_PT
dc.subjectImmunoglobulinpt_PT
dc.subjectJuvenile idiopathic arthritispt_PT
dc.subjectSubcutaneous Immunoglobulinpt_PT
dc.subjectVaccine Associated Paralytic Poliomyelitispt_PT
dc.subjectXLA, X-Linked Agammaglobulinemiapt_PT
dc.subjectHDE PEDpt_PT
dc.titleX-Linked Agammaglobulinemia (XLA):Phenotype, Diagnosis, and Therapeutic Challenges Around the Worldpt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.issue3pt_PT
oaire.citation.startPage100018pt_PT
oaire.citation.volume12pt_PT
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT

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